Therapy in Pediatric Dermatology Management of Pediatric Skin Disease 1st Edition by Joyce M.C. Teng, Ann L. Marqueling, Latanya T. Benjamin – Ebook PDF Instant Download/DeliveryISBN: 3319436287, 9783319436289
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ISBN-10 : 3319436287
ISBN-13 : 9783319436289
Author: Joyce M.C. Teng, Ann L. Marqueling, Latanya T. Benjamin
This book addresses the need for comprehensive review of therapeutic options that are known to be efficacious in the management of cutaneous diseases in children. It summarizes evidence-based literature on clinical responses among pediatric patients, including age-appropriate management strategies. Included is review of the extraordinary developments in understanding of the genetics and pathogenesis of many cutaneous disorders during the past decade, the novel therapeutic options and repurposing of old drugs, and the management of some of the most challenging skin disorders. Therapy in Pediatric Dermatology: Management of Pediatric Skin Disease is a succinct, user-friendly, and up-to-date therapeutic dermatologic textbook for physicians who care for children with skin disorders. Each skin condition is discussed with investigative and treatment recommendations in mind and provided based on extensive review of the literature. This book will provide unbiased, yet concise, information that is valuable to practitioners who manage pediatric patients in their practices.
Therapy in Pediatric Dermatology Management of Pediatric Skin Disease 1st Table of contents:
1: Overview of Dermatologic Care in Children
Skin Care of Normal Newborn Skin
Clinical Features
Management Strategies
Investigations Recommended [3]Therapies [3, 6, 9, 11]Therapies: Daily Umbilical Cord Care [6]Principles of Pediatric Skin Care
Clinical Features
Management Strategies
Investigations Recommended
Premature Skin
Clinical Features
Management Strategies
Investigations Recommended [3, 6]Therapies: Daily Umbilical Cord Care [6]Therapies [3, 6, 8, 9]Special Considerations for Newborn Skin
Clinical Features
Investigations Recommended
Management Strategies
Skin Care Products to Avoid
Clinical Features
Management Strategies
References
2: Management of Skin Disorders of the Newborn
Evidence Level
Neonatal Cephalic Pustulosis
Neonatal/Infantile Acne (Fig. 2.1)
For Severe Acne Consider
Seborrheic Dermatitis
Acrodermatitis Enteropathica
Acropustulosis of Infancy
Aplasia Cutis Congenita [14] (Figs. 2.2 and 2.3)
Bronze Baby Syndrome
Congenital/Neonatal Herpes Simplex Virus (HSV)
Congenital/Neonatal Candidiasis
Staphylococcus Aureus Pustulosis (Fig. 2.4)
Neonatal Scabies (Fig. 2.5)
Cutis Marmorata Telangiectatica Congenita (Figs. 2.6 and 2.7)
Eosinophilic Pustular Folliculitis (Fig. 2.8)
Granuloma Gluteale Infantum (Fig. 2.9)
Sclerema Neonatorum
Subcutaneous Fat Necrosis [56, 57]References
3: Atopic Dermatitis and Eczematous Eruptions
Atopic Dermatitis
Clinical Features of the Disorder
Management Strategies
Treatment Overview
Clearance Phase
Maintenance Phase
Rescue of Flares
Adjunctive Interventions
Refractory Disease
Specific Investigations Recommended
Pityriasis Alba
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended
Contact Dermatitis
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended [46–49]Juvenile Plantar Dermatosis
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended [59]Lichen Simplex Chronicus
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended
Lichen Striatus
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended
Nummular Dermatitis (Discoid Eczema)
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended [83–86]Seborrheic Dermatitis
Clinical Features of the Disorder
Management Strategies
Specific Investigations Recommended
References
4: Psoriasis and Other Papulosquamous Skin Disorders
Psoriasis
Clinical Features
Management Strategies
Investigations Recommended
Reactive Arthritis
Clinical Features
Management Strategies
Investigations Recommended
Pityriasis Rubra Pilaris
Clinical Features
Management Strategies
Investigations Recommended
Pityriasis Lichenoides
Clinical Features
Management Strategies
Investigations Recommended
Lymphomatoid Papulosis
Clinical Features
Management Strategies
Investigations Recommended
Pityriasis Rosea
Clinical Features
Management Strategies
Investigations Recommended
Lichen Planus
Clinical Features
Management Strategies
Investigations Recommended
Lichen Nitidus
Clinical Features
Management Strategies
Investigations Recommended
Keratosis Lichenoides Chronica
Clinical Features
Management Strategies
Investigations Recommended
References
5: Hereditary Disorders of Cornification
Introduction
Classification of the Ichthyoses and Other DOC
Management Strategies for DOC
Investigations for Diagnosis
General Approach to Therapy in Children
Specific Therapies
Emollients
Keratolytics
Antimicrobials
Baths
Physical Treatment
Retinoids
Topical Retinoids
Oral Retinoids
Retinoic Acid Metabolism Blocking Agent (RAMBA)
Targeted Therapy
Distinctive Features and Therapeutic Ladders for Selected DOC
Non-Syndromic Disorders: Autosomal Recessive Congenital Ichthyosis (ARCI), Epidermolytic Ichthyosis
Epidermolytic Ichthyosis (EI)
Management Strategies
Investigations Recommended
Autosomal Recessive Congenital Ichthyosis (ARCI)
Investigations Recommended
Erythrokeratodermia Variabilis
Management Strategies
Investigations Recommended
Syndromic Disorders: Netherton and Sjogren-Larsson Syndromes
Netherton Syndrome (NS)
Management Strategies
Investigations Recommended
Sjogren-Larsson Syndrome
Management Strategies
Investigations Recommended
Other Disorders of Differentiation: Darier Disease, Palmoplantar Keratodermas
Darier Disease
Management Strategies
Investigations Recommended
Palmoplantar Keratodermas
Management Strategies
Investigations Recommended
References
6: Hereditary Disorders of the Dermis
Ehlers Danlos Syndrome
Clinical Features
Management Strategies
Specific Investigations Recommended [4]First Line Therapies
Marfan Syndrome
Clinical Features
Management Strategies
Specific Investigations Recommended
First Line Therapies
Second Line Therapies
Surgical Considerations
Cutis Laxa
Clinical Features
Management Strategies
First Line Therapies
Pseudoxanthoma Elasticum
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Second Line Therapies
Elastosis Perforans Serpiginosa
Clinical Features
Management Strategies
Specific Investigations Recommended
First Line Therapies
Second Line Therapies
Focal Dermal Hypoplasia
Clinical Features
Management Strategies
Specific Investigations Recommended
First Line Therapies
Second Line Therapies
Third Line Therapies
Buschke-Ollendorff Syndrome
Clinical Features
Management Strategies
Specific Investigations Recommended
Hutchinson-Gilford Progeria Syndrome
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Second Line Therapies
Werner Syndrome
Clinical Features
Management Strategies
Specific Investigations Recommended
First Line Therapies
Second Line Therapies
Lethal Restrictive Dermopathy
Clinical Features
Management Strategies
Specific Investigations Recommended
Stiff Skin Syndrome
Clinical Features
Management Strategies
Specific Investigations Recommended
First Line Therapies
Lipoid Proteinosis
Clinical Features
Management Strategies
Specific Investigations Recommended
First Line Therapies
Second Line Therapies
Infantile Systemic Hyalinosis and Juvenile Hyaline Fibromatosis
Clinical Features
Management Strategies
Specific Investigations Recommended
For Diagnosis
First Line Therapies
Second Line Therapies
Osteogenesis Imperfecta
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Second Line Therapies
Third Line Therapies
Winchester Syndrome
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
References
7: Disorders of Hair and Nail
Congenital Non-scarring Alopecias with Fragility
Overview
Investigations Recommended
For Diagnosis
For Treatment
Trichorrhexis Invaginata (Bamboo Hair)
Clinical Features
Monilethrix (Beaded Hair; MIM158000, 177750, 252700)
Clinical Features
Investigations Recommended
For Diagnosis
Menkes Kinky Hair Syndrome (MIM 309400)
Clinical Features
Trichothiodystrophy (MIM 601675)
Clinical Features
Congenital Hair Shaft Disorders Without Fragility
Diffuse Partial Woolly Hair (DPWH)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
First Line Therapies
Pili Annulati (MIM 180600)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Woolly Hair
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Uncombable Hair Syndrome (Pili Trianguli et Canaliculi, Spun Glass Hair)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Acquired Hair Shaft Disorders Without Fragility
Acquired Progressive Kinking of the Hair (APKH)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
First Line Therapies
Alopecia Areata (AA)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
First Line Therapies
Second Line Therapies
Third Line Therapies
Loose Anagen Hair Syndrome (LAHS)
Clinical Features
Investigations Recommended
For Diagnosis
Short Anagen Hair Syndrome
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Scarring Alopecia
Keratosis Follicularis Spinulosa Decalvans (MIM 308800)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Eruptive Vellus Hair Cysts (EVHC)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Hypertrichosis
Clinical Features
Generalized Hypertrichosis
Congenital Hypertrichosis Universalis (MIM 145701)
Congenital Hypertrichosis Lanuginosa (MIM 145700, 307150)
Prepubertal Hypertrichosis
Localized Hypertrichosis
Congenital Melanocytic Nevi
Becker’s Nevus
Hypertrichosis Cubiti (Hairy Elbows Syndrome)
Cervical Hypertrichosis
Faun Tail (Lumbosacral Hypertrichosis; Spinal Hypertrichosis)
Hypertrichois in Porphyria
Trichomegaly
Acquired Hypertrichosis
Drug-Induced Hypertrichosis
Postinflammatory/Post-traumatic Hypertrichosis
Investigations Recommended
For Diagnosis
For Treatment
First Line Therapies
Second Line Therapies
Hirsutism
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
First Line Therapies
Nail Disorders
Twenty-Nail Dystrophy (TND, Trachyonychia)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Pachyonychia Congenital (PC)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Congenital Malalignment of the Big Toenail
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Ingrown Nails (Unguis Incarnates, Onychocryptosis)
Clinical Features
Investigations Recommended
For Diagnosis
Treatment
Beau’s Lines
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
Onychomadesis (Nail Shedding)
Clinical Features
Investigations Recommended
For Diagnosis
For Treatment
References
8: Disorders of the Sebaceous and Sweat Gland
Clinical Features of Acne Vulgaris and Its Variants
Acne Vulgaris
Acne Fulminans
Acne Conglobata
Drug-Induced Acne
Specific Investigations
Discussion of Treatment Modalities
Topical Retinoids
Topical Antimicrobials
Other Topical Agents
Oral Antibiotics
Isotretinoin
Oral Dapsone
Hormonal Therapy
Neonatal Acne
Specific Investigations
Infantile Acne
Specific Investigations
Mid-childhood Acne
Specific Investigations
Preadolescent Acne
Specific Investigations
Periorificial Dermatitis
Specific Investigations
Childhood Rosacea
Specific Investigations
Keratosis Pilaris
Specific Investigations
Pseudoacne of the Nasal Crease
Specific Investigations
Demodicosis
Specific Investigations
Idiopathic Facial Aseptic Granuloma
Specific Investigations
References
9: Cutaneous Tumor and Tumor Syndromes
Pigmented Lesions: Congenital Melanocytic Nevus
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Second Line Therapies
Spitz Nevus
Management Strategies
Specific Investigations
Halo Nevus
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Becker’s Melanosis
Clinical Features
Management Strategies
Investigations Recommended
Tumor of the Epidermal Appendages: Nevus Comedonicus
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Second Line Therapies
Third Line Therapies
Nevus Sebaceous
Clinical Features
Management Strategies
Investigations Recommended
First Line Therapies
Second Line Therapies
Other Adnexal Tumors
Clinical Features
Management
Investigations Recommended
First Line Therapies
Second Line Therapies
Tumor of the Epidermis: Mastocytosis
Clinical Features
Management Strategies
Investigations Recommended
Basal Cell Nevus Syndrome
Clinical Features
Management
Investigations Recommended
First Line Therapies
Second Line Therapies
Third Line Therapies
Epidermal Nevus and Epidermal Nevus Syndrome
Clinical Features
Management
Investigations Recommended
First Line Therapies
Second Line Treatments
Dermal Tumor: Angiofibroma
Clinical Features
Management Strategies
Investigations Recommended
Connective Tissue Nevus
Clinical Features
Management Strategies
Investigations Recommended
Granuloma Annulare
Clinical Features
Management Strategies
Investigation Recommended
Neurofibroma
Clinical Features
Management Strategies
Investigations Recommended
Dermatofibrosarcoma Protuberans
Clinical Features
Management Strategies
Investigations Recommended
Fibromatoses: Recurring Digital Fibroma of Childhood
Clinical Features
Management Strategies
Investigations Recommended
Infantile Myofibromatosis
Clinical Features
Management Strategies
Investigations Recommended
Tumors of the Oral Mucosa: Congenital Granular Cell Tumor
Clinical Features
Management Strategies
Investigations Recommended
Mucocele
Clinical Features
Management Strategies
Investigations Recommended
Miscellaneous: Epidermal Cyst
Clinical Features
Management Strategies
Investigations Recommended
Steatocystoma Multiplex
Clinical Features
Management Strategies
Investigations Recommended
Calcinosis Cutis
Clinical Features
Management Strategies
Investigations Recommended
Osteoma Cutis
Clinical Features
Management Strategies
Investigations Recommended
Summary
References
10: Histiocytoses and Malignancy
Langerhans Cell Histiocytosis
Clinical Features
Management Strategies
Investigations Recommended
Juvenile Xanthogranuloma
Clinical Features
Investigation Recommendations
Management Strategies
Cutaneous Disease
Ocular Disease
Visceral Lesions
Benign Cephalic Histiocytosis
Clinical Features
Investigation Recommendations
Management Strategies
Xanthoma Disseminatum
Clinical Features
Investigation Recommendations
Management Strategies
Necrobiotic Xanthogranuloma
Clinical Features
Investigation Recommendations
Management Strategies
Generalized Eruptive Histiocytoma
Clinical Features
Investigation Recommendations
Management Strategies
Progressive Nodular Histiocytoma
Clinical Features
Investigation Recommendations
Management Strategies
Multicentric Reticulohistiocytosis
Clinical Features
Investigation Recommendations
Management Strategies
Cutaneous Disease
Joint Disease
Sinus Histiocytosis with Massive LAD (Rosai-Dorfman Disease)
Clinical Features
Investigation Recommendations
Management Strategies
Leukemia Cutis
Clinical Features
Investigation Recommendations
Management Strategies
Cutaneous T-Cell Lymphomas
Clinical Features
Management Strategies
Investigations Recommended
References
Generalized Eruptive Histiocytoma
11: Disorders of Pigmentation
Introduction
Congenital Localized Alterations in Pigmentation
Mongolian Spot
Café au Lait Macules
Nevus Depigmentosus (Fig. 11.2)
Tuberous Sclerosis
Nevoid Melanosis or Blaschkoid Pigmentation
Becker’s Nevus
Nevus of Ito and Nevus of Ota
Congenital Widespread Alterations in Pigmentation
Oculocutaneous Albinism
Clinical Features
Investigations Recommended
Phenylketonuria
Clinical Features
Investigations Recommended
Silvery Hair Syndromes (Chediak-Higashi Syndrome, Griscelli Syndrome and Elejalde Syndrome)
Clinical Features
Investigations Recommended
Piebaldism
Clinical Features
Investigations Recommended
Waardenburg Syndrome
Clinical Features
Investigations Recommended
Acquired Localized Disorders of Pigmentation
Pityriasis Alba
Clinical Features
Investigations Recommended
Tinea Versicolor
Clinical Features
Investigations Recommended
Terre Firme
Post-Inflammatory Pigment Alteration (PIPA)
Acquired Generalized Disorders of Pigmentation
Acanthosis Nigricans
Investigations Recommended
Vitiligo
Investigations Recommended
References
12: Vascular Disorders and Anomalies
Vascular Tumors
Infantile Hemangioma
Clinical Features
Management Strategies
Investigations Recommended
Kasabach Merritt Phenomenon (KMP)
Clinical Features
Management Strategies
Investigations Recommended
Multifocal Lymphangioendotheliomatosis with Thrombocytopenia
Clinical Features
Management Strategies
Investigations Recommended
Pyogenic Granuloma
Clinical Features
Management Strategies
Investigations Recommended
Angiofibromas
Clinical Features
Management Strategies
Investigations Recommended
Vascular Malformations
Capillary Malformations
Clinical Features
Management Strategies
Investigations Recommended
Venous Malformations and Lymphatic Malformations
Clinical Features
Management Strategies
Investigations Recommended
Arteriovenous Malformations
Clinical Features
Management Strategies
Investigations Recommended
References
13: Genodermatoses and Basement Membrane Zone Diseases
Epidermolysis Bullosa (EB)
Specific Strategies
Investigations Recommended
Specific Therapies
Epidermolysis Bullosa Acquisita (EBA)
Management Strategies
Investigations
Ectodermal Dysplasia with Skin Fragility (EDSF)
Management Strategies
Investigations
Specific Therapies
Kindler Syndrome
Clinical Features
Management Strategies
Investigations
Specific Therapies
Pemphigus
Investigations
Pemphigus Vulgaris [9]Pemphigus Foliaceus/Erythematosus
Specific Therapies (For PV and PF)
Paraneoplastic Pemphigus
Investigations
Specific Therapies
Bullous Pemphigoid
Investigations
Specific Therapies
Dermatitis Herpetiformis
Management Strategies
Investigations
Specific Therapies
Chronic Bullous Disease of Childhood (CBDC)
Clinical Features (Fig. 13.6)
Investigations
Specific Therapies
Bullous Systemic Lupus Erythematosus (BSLE)
Criteria for BSLE
Investigations
Specific Thrapies
References
14: Infectious Diseases: Bacterial Infections
Staphylococcal and Streptococcal Infections
Clinical Features
Infections Mainly Caused by Staphylococcus aureus
Infections Mainly Caused by Streptococcus pyogenes
Specific Investigations
Impetigo and Ecthyma
Staphylococcal Folliculitis Including Folliculitis Barbae (Sycosis)
Furuncles and Carbuncles
Staphylococcal Scalded Skin Syndrome (SSSS)
Scarlet Fever
Perineal Streptococcal Dermatitis
Blistering Distal Dactylitis
Erysipelas
Cellulitis
Streptococcal Toxic Shock Syndrome (TSS)
Staphylococcal Toxic Shock Syndrome (TSS)
Necrotizing Fasciitis
Pseudomonas Infections
Clinical Features
Specific Investigations
Ecthyma Gangrenosum
Noma Neonatorum
Noma
Clinical Features
Specific Investigations
Neisseria Infections
Clinical Features
Specific Investigations
Disseminated Gonococcal Infection
Meningococcemia
Corynebacterial Infections
Clinical Features
Specific Investigations
Erythrasma
Pitted Keratolysis
Trichomycosis
Erysipeloid
Clinical Features
Specific Investigations
Anthrax
Clinical Features
Specific Investigations
Management Strategy
Adjunct therapies for cutaneous anthrax [198–203]Bartonella: Cat Scratch Disease
Clinical Features
Specific Investigations
Fungus-Like Bacteria: Actinomycosis and Nocardiosis
Clinical Features
Specific Investigations
Actinomycosis
Nocardiosis
Treponemal Infections
Clinical Features
Specific Investigations
Syphilis
Yaws, Pinta, and Bejel
Lyme Disease
Mycobacterial Infections
Clinical Features
Specific Investigations
Nontuberculous Mycobacterial Infections (Table 14.77)
Cutaneous Tuberculosis
Therapy for Drug-Susceptible Tuberculosis [325, 326]Therapy for Drug-Resistant Tuberculosis [325, 327–330]Leprosy
Therapies for Immunologic Reactions in Leprosy [343–351]Rickettsial Diseases with Cutaneous Manifestations
Clinical Features
Specific Investigations
References
15: Infectious Diseases: Leishmaniasis
Clinical Features
Management Strategy
Specific Investigations
References
16: Infectious Diseases: Superficial Fungal Infections
Dermatophytosis
Clinical Features
Specific Investigations
Tinea Capitis and Barbae
Management Strategy
Tinea Corporis, Faciei, and Cruris
Tinea Pedis and Manuum
Dermatophytic Onychomycosis (Tinea Unguium)
Management Strategy
Tinea Versicolor
Clinical Features
Specific Investigations [1, 2]Management Strategy
Tinea Nigra
Clinical Features
Specific Investigations
Management Strategy
Piedra
Clinical Features
Specific Investigations
White Piedra
Black Piedra
Candidiasis
Clinical Features
Specific Investigations
Oropharyngeal Candidiasis
Candidal Intertrigo and Diaper Dermatitis
Candidal Vulvovaginitis
Neonatal and Systemic Candidiasis
Management Strategies
Chronic Mucocutaneous Candidiasis
References
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